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Journal of Neurorestoratology  2020, Vol. 8 Issue (2): 83-92    doi: 10.26599/JNR.2020.9040010
Review Article     
Chinese expert consensus on diagnosis and management of split cord malformation
Bo Xiu1,*, Fuyun Liu2, Aijia Shang3, Rui Zhang4
1 Department of Neurosurgery, The 7th Medical Center of PLA General Hospital, Beijing 100700, China
2 Department of Pediatric Orthopaedics, Zhengzhou University The 3rd Hospital, Zhengzhou 450052, Henan, China
3 Department of Neurosurgery, The 1st Medical Center of PLA General Hospital, Beijing 100853, China
4 Department of Neurosurgery, Shandong Provincial Hospital Affiliated to Shandong First Medical University, Ji'nan 250021, Shandong, China
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Abstract  

Split cord malformation (SCM) is a neural tube defect that the spinal cord is longitudinally separated into two hemicords with individual functions, which causes severe spinal cord impairment and sensorimotor deficit. As a kind of myelodysplasia and a special type of tethered cord syndrome, SCM is not widely understood, and common issues in the diagnosis and treatment of SCM should be clarified. In this paper, the Chinese Split Cord Malformation Working Group made a consensus for SCM on embryopathogenesis and types, clinical presentations, neuroimaging assessment, indications and principle of the surgery, surgical techniques and nuances, and prognosis and follow up.



Key wordssplit cord malformation      tethered cord syndrome      neural tube defect      diagnosis      surgery      consensus     
Received: 26 April 2020      Published: 11 August 2020
Corresponding Authors: Bo Xiu   
Cite this article:

Bo Xiu, Fuyun Liu, Aijia Shang, Rui Zhang. Chinese expert consensus on diagnosis and management of split cord malformation. Journal of Neurorestoratology, 2020, 8: 83-92.

URL:

http://jnr.tsinghuajournals.com/10.26599/JNR.2020.9040010     OR     http://jnr.tsinghuajournals.com/Y2020/V8/I2/83

1Nan BoShanghai Children's Medical Center
2Qian ChenShenzhen Children's Hospital
3Ruoping ChenXinhua Hospital Affiliated to School of Medicine, Shanghai Jiaotong University
4Shuo GuHainan Women and Children's Medical Center
5Xiaosheng HeXijing Hospital of Air-force Military Medical University
6Wen JinShanxi Children's Hospital
7Cuicui LiThe 7th Medical Center of PLA General Hospital
8Fangcheng LiGuangzhou Women and Children's Medical Center
9Hao LiFudan University Children's Hospital
10Fuyun LiuZhengzhou University the Third Hospital
11Wei LiuBeijing Tiantan Hospital, Capital Medical University
12Lin QiChildren's Hospital Affiliated to Zhengzhou University
13Xiang QiBeijing Children's Hospital, Capital Medical University
14Aijia ShangThe First Medical Center of PLA General Hospital
15Zhipeng ShenThe Children's Hospital , Zhejiang University
16Hangyu ShiXi'an Children's Hospital
17Benzhang TaoThe First Medical Center of PLA General Hospital
18Feng WanTongji Hospital Affiliated to Huazhong University of Science & Technology
19Guangyu WangQilu Children's Hospital of Shandong University
20Jvlei WangTangdu Hospital of Air-force Military Medical University
21Linlin WangInstitute of Reproductive and Child Health, Peking University Health Science Center
22Shuihua WuHunan Children's Hospital
23Bo XiuThe 7th Medical Center of PLA General Hospital
24Zhi YuanThe Second Hospital of Lanzhou University
25Xuan ZhaiThe Children's Hospital, Chongqing Medical University
26Rui ZhangShandong Provincial Hospital Affiliated to Shandong First Medical University
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